Cleidocranial Dysostosis – An Enigma Developmental Bones Anomaly
A. O. Adebola Yusuf *
Department of Radiology, Benjamin Carson (Snr) School of Medicine, Babcock University Ilishan Remo, Ogun State, Nigeria.
A. Adeniyi
Department of Preventive Dentistry, Faculty of Dentistry, Lagos State University College of Medicine, Nigeria.
T. A. Oyedele
Department of Surgery, Benjamin Carson (Snr) School of Medicine, Babcock University Ilishan Remo, Ogun State, Nigeria.
C. O. Akisanya
Department of Rediology, Federal Medical Center, Abeokuta, Ogun State, Nigeria.
*Author to whom correspondence should be addressed.
Abstract
Cleidocranial Dysostosis, known also as Cleidocranial dysplasia, Mutational Dysostosis, Scheuthauer Marie-Sainton syndrome, is a rare condition which is characterized by delayed ossification of midline structures. Case study of the phenomenon has been reported here. Reports revealed that the classical association of a spectacular dental anarchy, with non-closure of cranial sutures, retention of deciduous teeth and delayed eruption of permanent denture and typical facies of underdevelopment raise strong suspicion of autosomal syndrome. The reviewed patient as a classic demonstration of cleidocranial dysostosis, succinctly represented the condition.
Keywords: Cleidocranial dysostosis, mutational dysostosis, case study