Hemoptysis in a Young Adult with Congenital Cystic Adenomatoid Malformation of the Lung: Case Report
Mohammed Salem
IBN Sina Medical College, Jeddah, KSA.
Abdulaziz Al-Ahmadi
Taibah University, Al-Madinah Al-Munawarah, KSA.
Basil Al-Ahmadi
Taibah University, Al-Madinah Al-Munawarah, KSA.
Ammar Dabbour
Taibah University, Al-Madinah Al-Munawarah, KSA.
Ahmed Al Hujaily
Histopathology Division, King Fahad Hospital, Al-Madinah Al-Munawarah, KSA.
Alsyed Rashad
Respiratory Division, King Fahad Hospital, Al-Madinah Al-Munawarah, KSA
Abeer Alharbi *
Respiratory Division, King Fahad Hospital, Al-Madinah Al-Munawarah, KSA.
*Author to whom correspondence should be addressed.
Abstract
Congenital cystic adenomatoid malformations (CCAM), also named congenital pulmonary airway malformation s (CPAM) are multicystic masses of segmental lung tissue with abnormal bronchial proliferation. There is failure of normal bronchoalveolar development with a hamartomatous proliferation of terminal respiratory units in a gland-like pattern (adenomatoid). CPAM can be divided into five types, according to clinical and pathologic features. [1] CPAM type 1 is the most common, and has good prognosis. The widespread use of antenatal ultrasound examination has resulted in an increase in the prenatal diagnosis of CPAM [2]. The diagnosis may not be made for many years or even until adulthood when the abnormality is small. With recurrent chest infection it does become apparent [3,4]. This case report documents young male patient with hemoptysis, and right lower lobe t variable sized cysts for which he underwent right thoracotomy with right lower lobectomy. The histopathology tissue report showed feature of congenital pulmonary airway malformation, Type 1(CPAM1).
Keywords: Hemoptysis, congenital cystic adenomatoid malformations.